International Journal of Cardiovascular Practice
Article in Press

Scimitar Syndrome Issued from a Consanguineous Marriage: A Rare Congenital Cardiomyopathy

Rihab Machtache (Department of Cardiology, Ibn Rochd University Teaching Hospital, Hassan II University, Casablanca, Morocco)
Soukaina Safir (Department of Cardiology, Ibn Rochd University Teaching Hospital, Hassan II University, Casablanca, Morocco)
Sara Chibane (Department of Cardiology, Ibn Rochd University Teaching Hospital, Hassan II University, Casablanca, Morocco)
Abdenasser Drighil (Department of Cardiology, Ibn Rochd University Teaching Hospital, Hassan II University, Casablanca, Morocco)
Leila Azzouzi (Department of Cardiology, Ibn Rochd University Teaching Hospital, Hassan II University, Casablanca, Morocco)
Rachida Habbal (Department of Cardiology, Ibn Rochd University Teaching Hospital, Hassan II University, Casablanca, Morocco)
Fadoua Kossale (Department of Radiology, Ibn Rochd University Teaching Hospital, Hassan II University, Casablanca, Morocco)
Pr Salam (Department of Radiology, Ibn Rochd University Teaching Hospital, Hassan II University, Casablanca, Morocco)



Article Info

Publish Date
15 Jun 2020

Abstract

We present here a rare case of Scimitar syndrome on a full-term newborn female issued from consanguineous marriage and diagnosed at the age of two months who was suffering from polypnea since the age of two weeks. She was admitted at the age of two months for polypnea, non-dysmorphic facies, healthy systemic arterial tension, regular pulse, but the family history raises that before her birth, two newborns respectively boy and girl died both at an early age with dilated cardiomyopathy. After hospitalization, we realized chest radiography, which has shown opaque right lung and suspicion of scimitar syndrome. After that, an echocardiogram was performed, showing severe hypoplasia of the right pulmonary artery with pulmonary hypertension. The Thoracic computed tomography confirmed the diagnosis by revealing hypoplasia of the right pulmonary artery with pulmonary arterial hypertension, right pulmonary hypoplasia (bilobar), and abnormal partial right pulmonary venous return toward the vena cava under the diaphragm.

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Journal Info

Abbrev

ijcp

Publisher

Subject

Medicine & Pharmacology

Description

International Journal of Cardiovascular Practice(IJCP) is an international quarterly journal dedicated to a broad spectrum of topics in cardiology. All manuscripts must be prepared in English, and are subject to a rigorous and fair peer-review process. Accepted papers will immediately appear online ...