Archives of The Medicine and Case Reports
Vol. 4 No. 1 (2023): Archives of The Medicine and Case Reports

Kartagener Syndrome: A Case Report

Herick Alvenus Willim (Department of Emergency Medicine, Dr. Agoesdjam General Hospital, Ketapang, Indonesia)
Dofi Pebriadi (Department of Emergency Medicine, Dr. Agoesdjam General Hospital, Ketapang, Indonesia)
Eva Lydia Munthe (Department of Pulmonology and Respiratory Medicine, Dr. Agoesdjam General Hospital, Ketapang, Indonesia)
Harie Cipta (Department of Cardiology and Vascular Medicine, Dr. Agoesdjam General Hospital, Ketapang, Indonesia)
Widi Mujono (Department of Radiology, Dr. Agoesdjam General Hospital, Ketapang, Indonesia)
Abdul Muin (Department of Otolaryngology-Head and Neck Surgery, Dr. Agoesdjam General Hospital, Ketapang, Indonesia)



Article Info

Publish Date
29 Jun 2022

Abstract

Kartagener syndrome (KS) is a rare autosomal recessive disorder characterized by a clinical triad of situs inversus, chronic sinusitis, and bronchiectasis. Impaired ciliary motility due to abnormal ciliary structure or function is the main pathophysiological problem in KS. A 38-year-old woman presented to our outpatient clinic with a productive cough, fever, and shortness of breath for 1 month. She has had recurrent episodes of respiratory tract infections since childhood. Clinical investigations revealed situs inversus, sinusitis, and bronchiectasis. She was diagnosed with KS and treated with antibiotics, mucolytics, bronchodilators, and chest physiotherapy. Patients with KS present with chronic recurrent respiratory tract infections due to ineffective mucociliary clearance. Early diagnosis is important to improve prognosis. The main goals in the management of KS are to prevent the progression of the disease, preserve pulmonary function, and improve quality of life.

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Journal Info

Abbrev

AMCR

Publisher

Subject

Health Professions Medicine & Pharmacology Nursing Public Health

Description

Archives of The Medicine and Case Reports (AMCR) is a broad scope journal aims to publish the most exciting Case studies/reports in Clinical and Medical Sciences. AMCR aims to provide an excellent platform for Clinical Practitioners, medical/ health practitioners, students, professionals, ...