Chronic Septic Granulomatosis Revealed in Adulthood by Respiratory Manifestations

Fatima Ezzahra Haouassia (Pulmonology Department, Ibn Rochd University Hospital, Casablanca, Morocco)
Khadija Chaanoun (Pulmonology Department, Ibn Rochd University Hospital, Casablanca, Morocco)
Nahid Zaghba (Pulmonology Department, Ibn Rochd University Hospital, Casablanca, Morocco)
Hanane Benjelloun (Pulmonology Department, Ibn Rochd University Hospital, Casablanca, Morocco)
Najiba Yassine (Pulmonology Department, Ibn Rochd University Hospital, Casablanca, Morocco)

Jurnal Profesi Medika: Jurnal Kedokteran dan Kesehatan
Vol 18 No 1 (2024): Jurnal Profesi Medika : Jurnal Kedokteran dan Kesehatan

Chronic septic granulomatosis is a rare genetic disease that affects the immune system. It is characterized by a primary immune deficiency that makes it more difficult for phagocytic cells (such as polymorphonuclear neutrophils, eosinophils, monocytes, and macrophages) to eradicate some harmful bacteria and fungi. It is considered an orphan disease because it affects less than 0.05% of a given population.