Diagnosis dan Tata Laksana Hydroa Vacciniforme

Reisa Reshinta (Department of Dermatology and Venereology, Faculty of Medicine, University of Indonesia - RSUPN dr. Cipto Mangunkusumo, Jakarta, Indonesia)
Githa Rahmayunita (Department of Dermatology and Venereology, Faculty of Medicine, University of Indonesia - RSUPN dr. Cipto Mangunkusumo, Jakarta, Indonesia)
Rahadi Rihatmadja (Department of Dermatology and Venereology, Faculty of Medicine, University of Indonesia - RSUPN dr. Cipto Mangunkusumo, Jakarta, Indonesia)
Rinadewi Astriningrum (Department of Dermatology and Venereology, Faculty of Medicine, University of Indonesia - RSUPN dr. Cipto Mangunkusumo, Jakarta, Indonesia)

Cermin Dunia Kedokteran
Vol 51 No 5 (2024): Kedokteran Umum

Hydroa vacciniforme (HV) is a rare photodermatoses with the most frequent onset in childhood. The exact pathogenesis of HV is still not known. This disease is a spectrum with almost similar clinical symptoms, but with a very different prognosis. Classic HV has the best prognosis, but affects the quality of life due to scar formation, while hydroa vacciniforme-like lymphoma (HVLL) is the variant with the worst prognosis. HV needs to be considered as a differential diagnosis, especially in childhood-onset photodermatoses. Classical HV must be distinguishes from hydroa vacciniforme-like lymphoproliferative disorders (HVLPD) because it is related to prognosis. There is still no consensus or guidelines on diagnosis and management for HV.