<![CDATA[Highlights: Grade III microtia and right-sided unilateral involvement were the most common findings among the 33 patients, with a notable predominance in males aged 10-14 years at first examination. Isolated hemifacial microsomia emerged as the most frequently associated syndrome, with common accompanying features including facial asymmetry, facial dysostosis, and musculoskeletal anomalies. Abstract Introduction: Microtia is a congenital malformation of the external ear that can occur as an isolated finding or as part of a syndrome. Research on microtia syndromes in Indonesia is still limited. Hence, the exact number of cases is unknown. Methods: This was a descriptive observational study using a retrospective design to characterize the phenotypes of microtia syndromes among patients admitted to the Department of Plastic Surgery, Universitas Airlangga Hospital, Surabaya, Indonesia, from 2018-2024. Results: Thirty-three patients met the inclusion criteria. Among the patients were males (66.67%). Most patients (33.33%) were 10 to 14 years old on first examination. Unilateral right-sided cases were predominant (66.67%). Grade III was the most frequently observed classification (54.55%). As many as 24.24% of the cases had a hearing problem. The most common syndrome found was isolated hemifacial microsomia (21.25%). Other accompanying characteristics were facial asymmetry (39.39%), facial dysostosis (24.24%), musculoskeletal anomalies (21.21%), cardiac anomalies (21.21%), oral cleft (18.18%), ophthalmological anomalies (18.18%), neurological anomalies (15.15%), speech impairments (9%), and urogenital anomalies (3%). Conclusion: This study found that the patient population was predominantly male. Most cases were unilateral right-sided. The most commonly reported syndrome was isolated hemifacial microsomia, while the most common characteristic anomaly associated with microtia was facial asymmetry.]]>
