Primitive Neuroectodermal Tumour of the Maxilla Sinistra Region

Maryam Fathima (Unit Pelayanan Onkologi Radiasi, Fakultas Kedokteran, Universitas Indonesia, RS dr. Cipto Mangunkusumo, Jakarta, Indonesia)
Sri Mutya Sekarutami (Unit Pelayanan Onkologi Radiasi, Fakultas Kedokteran, Universitas Indonesia, RS dr.Cipto Mangunkusumo, Jakarta, Indonesia)

Radioterapi & Onkologi Indonesia
Vol 10, No 1 (2019): VOLUME 10 NO.1 JANUARI 2019

Primitive neuroectodermal tumors (PNET) are a group of malignant tumors composed of small round cells of neuroectodermal origin that affect soft tissue and bone. PNET have a rare incidence, occurring usualy in children and adolescents, rarely in adults. In this case report are focus of Peripheral primitive neuroektodermal tumors. Peripheral primitive neuroectodermal tumors (PNETp) are a group of aggressive malignancies that most commonly present in multiple tissues and organs including kidney, adrenal, bladder, liver, small intestine, colon and rectum, with a preferred location within the chest area (thoracopulmonary region), in the limbs and around the spine, but rarely, in the head and neck area. Here we present a case of the maxilla sinistra PNETp in a 17-year-old girl and we discuss the clinical features, histopathological characteristics, diagnosis, and treatment.