Paediatrica Indonesiana
Vol 63 No 3 (2023): May 2023

Pulmonary arteriovenous malformation as a cause of exercise intolerance in children: a case report

Pierluigi Morreale (Unknown)
Veronica Notarbartolo (Università degli Studi di Palermo)
Giancarlo Allegro (Unknown)
Mario Giuseppe Vallone (Unknown)
Francesca Finazzo (Unknown)
Vincenzo Antona (Unknown)
Maria Fiorella Sanfilippo (Unknown)
Calogero Comparato (Unknown)



Article Info

Publish Date
27 Jun 2023

Abstract

Pulmonary arteriovenous malformations (PAVMs) in children are rare lesions characterized by abnormal low resistance vascular structures connecting a pulmonary artery to a pulmonary vein, resulting in an intrapulmonary right-to-left shunt. The insidious onset and variable signs and symptoms make diagnosis difficult, especially in children. PAVMs can be single or multiple, congenital or acquired, and up to 47-80% of cases are associated with hereditary hemorrhagic telangiectasia (HHT).

Copyrights © 2023






Journal Info

Abbrev

paediatrica-indonesiana

Publisher

Subject

Health Professions Medicine & Pharmacology

Description

Paediatrica Indonesiana is a medical journal devoted to the health, in a broad sense, affecting fetuses, infants, children, and adolescents, belonged to the Indonesian Pediatric Society. Its publications are directed to pediatricians and other medical practitioners or researchers at all levels of ...