Francesca Finazzo
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Pulmonary arteriovenous malformation as a cause of exercise intolerance in children: a case report Pierluigi Morreale; Veronica Notarbartolo; Giancarlo Allegro; Mario Giuseppe Vallone; Francesca Finazzo; Vincenzo Antona; Maria Fiorella Sanfilippo; Calogero Comparato
Paediatrica Indonesiana Vol 63 No 3 (2023): May 2023
Publisher : Indonesian Pediatric Society

Show Abstract | Download Original | Original Source | Check in Google Scholar | DOI: 10.14238/pi63.3.2023.208-12

Abstract

Pulmonary arteriovenous malformations (PAVMs) in children are rare lesions characterized by abnormal low resistance vascular structures connecting a pulmonary artery to a pulmonary vein, resulting in an intrapulmonary right-to-left shunt. The insidious onset and variable signs and symptoms make diagnosis difficult, especially in children. PAVMs can be single or multiple, congenital or acquired, and up to 47-80% of cases are associated with hereditary hemorrhagic telangiectasia (HHT).