Garuda - Garba Rujukan Digital

Sensorineural hearing loss in Bartter syndrome Zizlavsky, Semiramis; -, Fadilah; Soewento, Ronny; Airlangga, Tri Juda
Oto Rhino Laryngologica Indonesiana Vol 51, No 1 (2021): Volume 51, No. 1 January - June 2021
Publisher : PERHATI-KL

Show Abstract | Download Original | Original Source | Check in Google Scholar | DOI: 10.32637/orli.v51i1.445

Background: Bartter syndrome is a rare inherited case characterized by autosomal recessive and has few different types. Diagnosis is established by laboratory findings, namely hypokalemic metabolic alkalosis, and normotensive. Hearing loss indicates Bartter syndrome type IV. Purpose: To report a case of Bartter syndrome with delayed speech. Case report: A seven years old girl with delayed speech and recurrent hypokalemia was referred to the Otolaryngology Head and Neck Surgery Department, Dr. Cipto Mangunkusumo Hospital, in order to evaluate the hearing level and treatment needed. Based on the Otoacoustic Emission (OAE), Brainstem Evoked Response Audiometry (BERA), and Auditory State Steady Response (ASSR), the diagnosis was profound bilateral sensorineural hearing loss and proceeded with hearing aid and also speech occupational therapy. Clinical question: Is there a relationship between Bartter syndrome and the incidence of hearing loss? Review method: Literature review through PubMed, Cochrane, and EBSCO, using keywords such as the impacts of Bartter syndrome on hearing loss, and sensorineural hearing loss in Bartter syndrome case. Result: Following screening of double publication and based on clinical questions over the past five years, only one relevant literature was found. Conclusion: Audiological assessment should be done in all Bartter syndromeâ€™s cases. Early intervention and timely audiological rehabilitation could improve the quality of life of such children.ABSTRAK Latar belakang: Sindrom Bartter merupakan kasus jarang, yang diturunkan secara autosomal resesif dan terdiri atas beberapa tipe. Diagnosis ditegakkan berdasarkan temuan laboratorium yaitu hipokalemi, alkalosis metabolik dan tekanan darah normal. Adanya gangguan pendengaran merupakan sindrom Bartter tipe IV. Tujuan: melaporkan kasus Sindrom Bartter dengan keterlambatan bicara. Kasus: Dilaporkan satu kasus anak perempuan berusia tujuh tahun dengan gangguan bicara dan terdapat riwayat hipokalemia berulang yang dirujuk ke Departemen Telinga Hidung Tenggorok-Bedah Kepala Leher, Rumah Sakit Cipto Mangunkusumo untuk menilai ambang dengar serta tatalaksana selanjutnya. Berdasarkan hasil pemeriksaan Otoacoustic Emission (OAE), Brainstem Evoked Response Audiometry (BERA) dan Auditory State Steady Response (ASSR) ditemukan tuli sensorineural sangat berat bilateral yang kemudian ditatalaksana dengan pemakaian Alat Bantu Dengar dan terapi wicara dan okupasi. Pertanyaan klinis: Apakah ada hubungan antara sindroma Bartter dengan insidens gangguan pendengaran? Telaah literatur: Pencarian literatur melalui, PubMed, Cochrane dan EBSCO dengan kata kunci hubungan gangguan pendengaran pada sindrom Bartter, gangguan pendengaran sensorineural pada sindrom Bartter. Hasil: Setelah dilakukan skrining yakni publikasi ganda dan sesuai pertanyaan klinis dari lima tahun terakhir hanya didapatkan satu literatur yang relevan. Kesimpulan: Pemeriksaan pendengaran harus dilakukan pada kasus dengan sindrom Bartter. Intervensi dini dan rehabilitasi audiologi yang tepat waktu dapat meningkatkan kualitas hidup anak dengan sindrom Bartter.Kata kunci: sindroma Bartter, tuli sensorineural.

Management of otosclerosis with obliterated footplate and round window involvement Priyono, Harim; Sari, Anita Amalia; Zizlavsky, Semiramis; Alviandi, Widayat; Ranakusuma, Respati W.
Oto Rhino Laryngologica Indonesiana Vol. 52 No. 2 (2022): VOLUME 52, NO. 2 JULY - DECEMBER 2022
Publisher : PERHATI-KL

Show Abstract | Download Original | Original Source | Check in Google Scholar | DOI: 10.32637/orli.v52i2.448

ABSTRACTBackground: Otosclerosis with obliterated footplate describes a condition with an overgrowth of bone so that the oval window is almost indistinguishable from the surrounding area. The occurence of round window obliteration is uncommon. In such cases, surgery is more difficult to perform and the results are often unsatisfactory. Purpose: To find out the management option for obliterative otosclerosis. Case report: A 35-year-old-man with suspected bilateral otosclerosis. The patient underwent transcanal endoscopic stapes surgery of the left ear with large fenestra stapedotomy procedure. Clinical question: In adult patients with obliterative otosclerosis, does stapes surgery improve hearing function and reduce complication? Review method: Using PubMed, EBSCOhost, Scopus and Proquest to search for the evidence of randomised control trial (RCT), cohort and case-control studies. Critical appraisal was conducted using critical appraisal tools from Center for Evidence Based Medicine (CEBM), Oxford University and qFAITH for systematic review/meta-analysis. Result: The literature searching used eligibility criteria based on keywords from clinical question found one study regarding the evaluation of intra-operative factors in otoslecrosis surgery outcomes, which was relevant to our clinical question. Conclusion: Large fenestra stapedotomy or stapedectomy is the preferred surgical technique for the management of obliterative otosclerosis. The involvement of round window caused a sensorineural hearing loss (SNHL) component and has a worse prognosis of hearing outcome post operatively. A further study is required to assess the best management for obliterative otosclerosis. ABSTRAKLatar belakang: Otosklerosis dengan obliterasi footplate menggambarkan suatu kondisi pertumbuhan tulang yang berlebihan sehingga tingkap lonjong hampir tidak dapat dibedakan dengan daerah sekitarnya. Obliterasi sampai ke tingkap bundar jarang terjadi. Hal tersebut menyebabkan operasi lebih sulit dilakukan dan hasilnya seringkali tidak memuaskan. Tujuan: Untuk mengetahui pilihan tatalaksana otosklerosis obliteratif. Laporan kasus: Laki-laki 35 tahun dengan suspek otosklerosis bilateral. Pasien menjalani operasi stapes telinga kiri dengan pendekatan endoskopi transkanal menggunakan prosedur stapedotomi fenestra besar. Pertanyaan klinis: Pada pasien dewasa dengan otosklerosis obliteratif, apakah operasi stapes dapat memulihkan fungsi pendengaran dan mengurangi komplikasi? Telaah literatur: Pencarian bukti melalui database PubMed, EBSCOhost, Scopus dan Proquest. Untuk uji coba kontrol acak, kohort dan studi kasus-kontrol, penilaian kritis dilakukan dengan menggunakan penilaian kritis dari CEBM, Oxford University dan qFAITH untuk tinjauan sistematis/meta-analisis. Hasil: Penelusuran literatur berdasarkan kriteria dari pertanyaan klinis, didapati satu artikel mengenai evaluasi faktor-faktor intraoperatif yang relevan dengan pertanyaan klinis. Kesimpulan: Stapedotomi fenestra besar atau stapedektomi adalah teknik bedah yang lebih dipilih untuk tatalaksana otosklerosis obliteratif. Keterlibatan tingkap bundar menyebabkan komponen gangguan pendengaran sensorineural, dan memiliki prognosis hasil pendengaran pasca operasi yang kurang baik. Dibutuhkan studi lebih lanjut untuk menilai tentang penatalaksanaan terbaik untuk kasus otosklerosis obliteratif.

Lennox-Gastaut syndrome and its impact on quality of life: hearing and speech perspective Zizlavsky, Semiramis; Putri, Shally Adhina Adhina; Pamungkas, Indra Parmaditya; Anam, Khoirul; Mangunatmadja, Irawan
Oto Rhino Laryngologica Indonesiana Vol. 52 No. 1 (2022): VOLUME 52, NO. 1 JANUARY - JUNE 2022
Publisher : PERHATI-KL

Show Abstract | Download Original | Original Source | Check in Google Scholar | DOI: 10.32637/orli.v52i1.549

ABSTRACTBackground: Lennox-Gastaut syndrome (LGS) is a severe pediatric epilepsy syndrome characterized by multiple seizure types including tonic, atonic, atypical absence, and generalized tonic-clonic seizures. LGS is also associated with cognitive decline and various neural disturbance, including hearing loss. Purpose: To report a case of Lennox-Gastaut syndrome with unilateral hearing loss and delayed speech. Case report: Four years old boy with LGS and delayed speech was referred to the Otolaryngology Outpatient Clinic, Dr Cipto Mangunkusumo Hospital for hearing and speech ability evaluation. He had had repeated seizures since he was three weeks old, and also had cortical lesion and mild atrophy in the left hemisphere brain. Hearing tests with Otoacoustic Emission (OAE), Brainstem Evoked Response Audiometry (BERA), and Auditory Steady State Response (ASSR) revealed profound unilateral hearing loss in the left ear, which required hearing aid and also speech therapy. Clinical question: Is there any correlation between brain abnormality/damage with unilateral hearing loss and delayed speech in Lennox-Gastaut syndrome? Method: Using Pubmed, Proquest Database, and Hand Searching to search the evidence. The evidence selected will be appraised by at least two members of our group using Oxford Center of Evidence-Based Medicine (CEBM) worksheet. Result: Following screening of double publication and its suitability to our clinical questions over ten years, no literature was found. Conclusion: The patient was given antiepileptic drugs (AEDs) and postural control training. For the hearing and speech problems, as the best comprehensive treatment the patient was suggested to use hearing aids and undergo speech therapy program. ABSTRAKLatar belakang: Lennox-Gastaut syndrome (LGS) adalah kumpulan gejala epilepsi berat pada anak dengan ciri khas kejang multipel, tonik, atonik, kejang absans atipik dan tonik klonik menyeluruh. LGS juga berkaitan dengan penurunan kognitif dan berbagai gangguan saraf, termasuk gangguan pendengaran. Tujuan: melaporkan kasus sindrom Lennox-Gastaut dengan gangguan pendengaran satu sisi dan keterlambatan bicara. Laporan Kasus: Seorang anak laki-laki berusia 4 tahun dengan sindroma Lennox-Gastaut mengalami keterlambatan bicara dirujuk ke Departemen Telinga Hidung Tenggorok, Rumah Sakit Dr.Cipto Mangunkusumo untuk evaluasi ambang dengar dan penanganannya. Riwayat penyakit menunjukkan kejang berulang sejak berusia tiga minggu, yang ditemukan juga lesi di korteks serebri dan atrofi ringan pada hemisfer otak kiri. Berdasarkan Otoacoustic Emission (OAE), Brainstem Evoked Response Audiometry (BERA), dan Auditory Steady State Response (ASSR) ditemukan adanya gangguan pendengaran sangat berat unilateral pada telinga kiri dan membutuhkan Alat Bantu Dengar dan terapi wicara. Pertanyaan klinis:Apakah terdapat korelasi antara abnormalitas otak atau kerusakan otak dengan gangguan pendengaran unilateral dan keterlambatan bicara pada LGS? Metode: Pencarian bukti dilakukan melalui PubMed, Proquest, dan pencarian manual. Artikel yang didapatkan kemudian ditelaah oleh setidaknya dua anggota kelompok dengan menggunakan lembar kerja yang diperoleh dari Oxford Center of Evidence-Based Medicine (CEBM) Hasil: Setelah dilakukan skrining publikasi ganda dan kesesuaian dengan pertanyaan klinis dari sepuluh tahun terakhir tidak ditemukan literatur yang sesuai. Kesimpulan: Pasien ditangani dengan obat antiepilepsi dan latihan psikomotorik. Untuk gangguan pendengaran pasien dianjurkan untuk menggunakan Alat bantu Dengar dan terapi wicara. Penanganan kasus LGS harus menyeluruh untuk memperoleh hasil yang baik.

Financing hearing aids for patients with congenital deafness in Indonesia Zachreini, Indra; Bashiruddin, Jenny; Zizlavsky, Semiramis; Tamin, Susyana; Priyono, Harim; Mayangsari, Ika Dwi; Alviandi, Widayat; Supartono, Natasha; Soetjipto, Damayanti; Ranakusuma, Respati; Damayanti, Heditya; Alia, Dina; Hajar Haryuna, Tengku Siti; Harahap, Juliandi; Warto, Nirza; Fitria, Hidayatul
Oto Rhino Laryngologica Indonesiana Vol. 52 No. 1 (2022): VOLUME 52, NO. 1 JANUARY - JUNE 2022
Publisher : PERHATI-KL

Show Abstract | Download Original | Original Source | Check in Google Scholar | DOI: 10.32637/orli.v52i1.550

ABSTRACTBackground: The appropriate management of patients with congenital deafness is installing hearing aids, either external hearing aids or implanted in the ear (cochlear implant), aiming to reduce the medical and social burden, besides improving the quality of life of the sufferers. Objective: To ascertain the cost of hearing aids in patients with congenital deafness, in the form of external hearing aids or cochlear implants. Method: A descriptive study with cross-sectional design using questionnaires through interviews. The sample size was 535 mothers whose children had congenital deafness at 24 hospitals with facilities for establishing a diagnosis of congenital deafness in 17 provinces in Indonesia. Result: Most respondents were aged 30-39 years (55%), occupations were housewives (71.8%), and education level was high school (52.5%). The type of hearing aid used mostly was external (92.7%), with 45.9% paid by personal expense. The surgically planted hearing aids in 22 children was mostly cochlear implants (95.5%), which were financed by the Indonesian Healthcare and Social Security Agency (BPJS) plus personal costs (50%). Discussion: This study found that the most common type of hearing aid used by children with hearing impairments was external hearing aids (92.7%) through independent financing (45.9%). Only 7.3% of patients chose surgery in hearing habilitation, and 95.5% were cochlear implants. The small percentage of surgery were due to the high-priced of cochlear implants, and the government did not cover all financial expenses. Conclusion: Most external hearing aids were paid independently-out-of-pocket, while cochlear implant surgeries were funded by BPJS, plus extra costs independently. ABSTRAKLatar belakang: Penatalaksanaan terbaik untuk penderita tuli kongenital adalah pemasangan alat bantu dengar (ABD), baik berupa ABD eksternal maupun ABD yang ditanam dalam telinga (implan koklea), dengan tujuan untuk mengurangi beban medis dan sosial, serta meningkatkan kualitas hidup penderita. Tujuan: Untuk mengetahui seberapa besar biaya pemasangan ABD pada penderita tuli kongenital, baik berupa ABD eksternal maupun implan koklea. Metode: Penelitian deskriptif dengan rancangan cross sectional study menggunakan kuesioner melalui wawancara. Besar sampel 535 ibu yang anaknya menderita tuli kongenital pada 24 rumah sakit yang memiliki fasilitas penegakkan diagnosis tuli kongenital di 17 provinsi di Indonesia. Hasil: Sebagian besar responden berusia 30-39 tahun (55%), pekerjaan terbanyak adalah ibu rumah tangga (71.8%), dan tingkat pendidikan SMA (52.5%). Jenis ABD yang terbanyak adalah ABD eksternal (92,7%) dengan pembiayaan secara mandiri 45,9%. Pemasangan ABD dengan tindakan operasi dilakukan pada 22 anak, yang terbanyak adalah implan koklea (95,5%) yang dibiayai oleh Badan Penyelenggara Jaminan Sosial (BPJS) ditambah dengan biaya sendiri (50%). Diskusi: Penelitian ini mendapati bahwa ABD yang terbanyak digunakan oleh anak dengan gangguan pendengaran adalah ABD eksternal (92,7%) dengan biaya mandiri (45,9%). Habilitasi pendengaran dengan tindakan operasi hanya dilakukan pada 7,3% pasien, berupa implantasi koklea 95,5%. Kecilnya persentase habilitasi bedah dikarenakan tingginya harga implant koklea, dan bantuan dari BPJS tidak meliputi keseluruhan biaya. Kesimpulan: Sebagian besar pembiayaan alat bantu dengar eksternal secara mandiri, sedangkan operasi implan koklea menggunakan biaya BPJS ditambah biaya sendiri.

Sensorineural hearing loss in a child with congenital hypothyroidism receiving thyroid hormone replacement therapy Zizlavsky, Semiramis; Handayani, Tri; Suwento, Ronny; Safitri, Eka Dwi; Airlangga, Tri Juda
Oto Rhino Laryngologica Indonesiana Vol. 52 No. 2 (2022): VOLUME 52, NO. 2 JULY - DECEMBER 2022
Publisher : PERHATI-KL

Show Abstract | Download Original | Original Source | Check in Google Scholar | DOI: 10.32637/orli.v52i2.580

ABSTRACTBackground: Congenital hypothyroidism remains as one of the most common causes of hearing loss in children, considering that thyroid hormone plays an essential role in the development and maturation of auditory organs. Purpose: To report a case of hearing loss in a child with congenital hypothyroidism who had received thyroid hormone replacement therapy. Case report: Presenting a 3-year-old boy with congenital hypothyroidism, growth and developmental delays, and a very severe bilateral sensorineural hearing loss. He was diagnosed at 6 months old, and even after subsequent therapies, the hearing impairment of the child remained profound. Clinical question: Could thyroid hormone replacement therapy improve the prognosis of hearing function in congenital hypothyroid patients accompanied by sensorineural hearing loss? Review method: Literature review through database PubMed, ProQuest, EBSCO, EBSCOhost and Embase, using keywords: “congenital hypothyroidism”, “hearing loss”, and “thyroid hormone replacement therapy”. Result: Screening on 1088 articles found no studies that were relevant with the clinical question and inclusion criteria. Conclusion: This report supported the evidence on the effects of congenital hypothyroidism on hearing loss, and the importance of early diagnosis and prompt treatment in congenital hypothyroid children. A missed diagnosis of congenital hypothyroidism in neonates may result in unfavorable effects on the child’s growth and development. Further studies are needed to assess the improvement of hearing function in congenital hypothyroid patients accompanied by sensorineural hearing loss that received thyroid hormone replacement therapy. ABSTRAKLatar belakang: Hipotiroidisme kongenital merupakan salah satu penyebab paling umum gangguan pendengaran pada anak-anak, terutama mengingat hormon tiroid berperan penting dalam perkembangan dan maturasi organ pendengaran. Tujuan: Melaporkan satu kasus gangguan pendengaran pada anak dengan hipotiroidisme kongenital yang menetap setelah terapi sulih hormon tiroid. Laporan kasus: Seorang anak laki-laki berusia 3 tahun dengan hipotiroidisme kongenital yang mengalami keterlambatan pertumbuhan dan perkembangan, dan gangguan pendengaran tipe sensorineural bilateral derajat sangat berat. Pasien didiagnosis pada usia 6 bulan, dan walaupun setelah terapi, gangguan pendengaran pada anak tersebut menetap. Pertanyaan klinis: Apakah terapi sulih hormon tiroid mempengaruhi prognosis perbaikan fungsi pendengaran pada pasien hipotiroid kongenital yang disertai gangguan pendengaran sensorineural? Tinjauan literatur: Melalui database PubMed, ProQuest, EBSCO, EBSCOhost dan Embase, menggunakan kata kunci: “hipotiroidisme kongenital”, “gangguan pendengaran”, “terapi sulih hormon tiroid”. Hasil: Setelah skrining 1088 artikel, tidak ada penelitian yang sesuai dengan pertanyaan klinis dan kriteria inklusi. Kesimpulan: Laporan ini menambah bukti tentang efek hipotiroidisme kongenital pada gangguan pendengaran, serta pentingnya diagnosis dini dan pengobatan segera pada anak hipotiroid kongenital. Diagnosis hipotiroidisme kongenital yang tidak terdeteksi pada neonatus, dapat mengakibatkan efek buruk pada pertumbuhan dan perkembangan anak. Diperlukan penelitian lebih lanjut untuk menilai prognosis peningkatan fungsi pendengaran pada pasien hipotiroid kongenital dengan gangguan pendengaran sensorineural, yang mendapatkan terapi sulih hormon tiroid.

Intraoperative Electrically Evoked Auditory Brainstem Response (eABR) examination in cochlear implant candidacy Zizlavsky, Semiramis; Saleh, Rangga Rayendra; Priyono, Harim
Oto Rhino Laryngologica Indonesiana Vol. 54 No. 1 (2024): VOLUME 54, NO. 1 JANUARY - JUNE 2024
Publisher : PERHATI-KL

Show Abstract | Download Original | Original Source | Check in Google Scholar | DOI: 10.32637/orli.v54i1.664

Background: Cochlear implantation is one of the most promising hearing habilitation methods for patients with profound sensorineural hearing loss (SNHL). One of the difficulties associated with the method is predicting the outcome of the surgery, especially in patients with cochlear nerve abnormalities. Purpose: To evaluate the intraoperative cochlear nerve response using Electrically Evoked Auditory Brainstem Response (eABR), and determine if cochlear implantation was required. Clinical question: How significant was intraoperative eABR in determining the outcome of cochlear implantation? Case report: This study considered two cases with profound bilateral SNHL that underwent intraoperative eABR. The first case involved 10-year-old girl who had used conventional hearing aids for eight years before surgery. She practiced lip reading for communication. The second case involved 4-year-old boy with delayed speech and a history of febrile seizure when he was two years old. He had used a conventional hearing aid for six months. Method: Evidence based literature was conducted through PubMed, Embase, and Wiley. Result: On the first case, eABR examination evoked no response in both ears and the parents decided not to carry on with the surgery. In the second case, eABR examination aroused a significant response in both ears, so the implantation was performed. Three months postoperative, the child was babbling and able to detect sound. Conclusion: eABR could give valuable input in identifying profound bilateral SNHL patients with cochlear nerve abnormality. The high cost of implant devices makes this examination beneficial for the patient’s family in deciding if implantation surgery is required. Keywords: cochlear implant, cochlear nerve hypoplasia, eABR, hearing habilitation, profound sensorineural hearing loss

Clinical approach to auditory malingering in an adolescent Yasin, Fikry; Zizlavsky, Semiramis; Irfan; Kaligis, Fransiska
Oto Rhino Laryngologica Indonesiana Vol. 54 No. 2 (2024): VOLUME 54, NO. 2 JULY - DECEMBER 2024
Publisher : PERHATI-KL

Show Abstract | Download Original | Original Source | Check in Google Scholar | DOI: 10.32637/orli.v54i2.640

Background: Cases of auditory malingering are frequently encountered in medical practice, but there was very limited scientific evidence on the characterization of auditory malingering in children and adolescents. Purpose: To provide a comprehensive description of an auditory malingering case in an adolescent. Case Report: A 14-year-old boy came with complaints of sudden bilateral deafness, for the last three months. Hearing examination findings were within normal limits. Discussion: An objective hearing examination was necessary to complement subjective assessments in establishing the diagnosis of hearing loss. In this case, following normal auditory findings and subsequent consultations, the patient admitted that he had feigned his symptoms to avoid bullying by his friends, who mocked him for never having visited Jakarta. Conclusion: The examination of hearing function should involve not only subjective hearing examinations, but also objective hearing examinations to establish a diagnosis of hearing loss. Keywords: hearing loss, hearing examination, malingering ABSTRAK Latar belakang: Kasus malingering yang melibatkan organ pendengaran cukup sering ditemukan dalam praktek kedokteran sehari-hari, namun bukti ilmiah yang mendeskripsikan kejadian malingering pendengaran pada anak-anak dan remaja masih sangat terbatas. Tujuan: Untuk menyampaikan secara komprehensif suatu kasus malingering pendengaran pada seorang remaja. Kasus: Laki-laki usia 14 tahun datang dengan keluhan mendadak tidak dapat mendengar pada kedua telinga sejak 3 bulan terakhir. Hasil pemeriksaan fungsi pendengaran dalam batas normal. Pembahasan: Pemeriksaan fungsi pendengaran secara obyektif diperlukan untuk menegakkan diagnosis gangguan pendengaran. Pada kasus ini, setelah temuan pendengaran yang normal dan konsultasi lanjutan, pasien mengaku telah memalsukan gejalanya untuk menghindari perundungan teman-temannya yang mengejeknya karena belum pernah mengunjungi Jakarta. Kesimpulan: Pemeriksaan fungsi pendengaran sebaiknya tidak hanya dilakukan pemeriksaan pendengaran subyektif saja, namun diperlukan juga pemeriksaan pendengaran obyektif untuk menegakkan diagnosis gangguan pendengaran. Kata kunci: gangguan pendengaran, pemeriksaan fungsi pendengaran, malingering

Tantangan Pasca Operasi Implan Koklea: Pengalaman 15 Tahun di Rumah Sakit Umum Pusat Nasional Cipto Mangunkusumo Zizlavsky, Semiramis; Priyono, Harim
Oto Rhino Laryngologica Indonesiana Vol. 55 No. 1 (2025): VOLUME 55, NO. 1 JANUARY - JUNE 2025
Publisher : PERHATI-KL

Show Abstract | Download Original | Original Source | Check in Google Scholar | DOI: 10.32637/orli.v55i1.701

Background: Hearing loss is a significant but often overlooked disability, particularly in developing countries as Indonesia, where access to specialized care is still limited. Purpose: To review the 15-years experience of cochlear implantation services at Cipto Mangunkusumo National General Hospital. Method: A retrospective study of children aged 0–18 years with profound hearing loss who underwent cochlear implant surgery between 2009 and 2023. Data were collected from medical records, including patient demographics, surgical outcomes, and complications. Result: A total of 255 patients (318 ears) received cochlear implants, with the majority aged 3–5 years (37.6%), and 54.5% male. Unilateral implants were predominant (75.3%). In 2020, a 92% decline in surgeries was noted due to the COVID-19 pandemic, which led to the postponement of elective and non-urgent cases. Post-surgical complications occurred in 4.3% of patients, with facial nerve stimulation being the most common side effects (36.4%). Conclusion: Despite expanding services, there still some obstacles remained, including high costs, limited access to specialized care, and unequal distribution of skilled professionals. Addressing these challenges is crucial to improving patient outcomes, and ensuring the sustainability of cochlear implant programs in Indonesia.

Clinical approach to auditory malingering in an adolescent Yasin, Fikry; Zizlavsky, Semiramis; Irfan, Irfan; Kaligis, Fransiska
Oto Rhino Laryngologica Indonesiana Vol. 54 No. 2 (2024): VOLUME 54, NO. 2 JULY - DECEMBER 2024
Publisher : PERHATI-KL

Show Abstract | Download Original | Original Source | Check in Google Scholar | DOI: 10.32637/orli.v54i2.640

Background: Cases of auditory malingering are frequently encountered in medical practice, but there was very limited scientific evidence on the characterization of auditory malingering in children and adolescents. Purpose: To provide a comprehensive description of an auditory malingering case in an adolescent. Case Report: A 14-year-old boy came with complaints of sudden bilateral deafness, for the last three months. Hearing examination findings were within normal limits. Discussion: An objective hearing examination was necessary to complement subjective assessments in establishing the diagnosis of hearing loss. In this case, following normal auditory findings and subsequent consultations, the patient admitted that he had feigned his symptoms to avoid bullying by his friends, who mocked him for never having visited Jakarta. Conclusion: The examination of hearing function should involve not only subjective hearing examinations, but also objective hearing examinations to establish a diagnosis of hearing loss. Keywords: hearing loss, hearing examination, malingering ABSTRAK Latar belakang: Kasus malingering yang melibatkan organ pendengaran cukup sering ditemukan dalam praktek kedokteran sehari-hari, namun bukti ilmiah yang mendeskripsikan kejadian malingering pendengaran pada anak-anak dan remaja masih sangat terbatas. Tujuan: Untuk menyampaikan secara komprehensif suatu kasus malingering pendengaran pada seorang remaja. Kasus: Laki-laki usia 14 tahun datang dengan keluhan mendadak tidak dapat mendengar pada kedua telinga sejak 3 bulan terakhir. Hasil pemeriksaan fungsi pendengaran dalam batas normal. Pembahasan: Pemeriksaan fungsi pendengaran secara obyektif diperlukan untuk menegakkan diagnosis gangguan pendengaran. Pada kasus ini, setelah temuan pendengaran yang normal dan konsultasi lanjutan, pasien mengaku telah memalsukan gejalanya untuk menghindari perundungan teman-temannya yang mengejeknya karena belum pernah mengunjungi Jakarta. Kesimpulan: Pemeriksaan fungsi pendengaran sebaiknya tidak hanya dilakukan pemeriksaan pendengaran subyektif saja, namun diperlukan juga pemeriksaan pendengaran obyektif untuk menegakkan diagnosis gangguan pendengaran. Kata kunci: gangguan pendengaran, pemeriksaan fungsi pendengaran, malingering

Intraoperative Electrically Evoked Auditory Brainstem Response (eABR) examination in cochlear implant candidacy Zizlavsky, Semiramis; Saleh, Rangga Rayendra; Priyono, Harim
Oto Rhino Laryngologica Indonesiana Vol. 54 No. 1 (2024): VOLUME 54, NO. 1 JANUARY - JUNE 2024
Publisher : PERHATI-KL

Show Abstract | Download Original | Original Source | Check in Google Scholar | DOI: 10.32637/orli.v54i1.664

Background: Cochlear implantation is one of the most promising hearing habilitation methods for patients with profound sensorineural hearing loss (SNHL). One of the difficulties associated with the method is predicting the outcome of the surgery, especially in patients with cochlear nerve abnormalities. Purpose: To evaluate the intraoperative cochlear nerve response using Electrically Evoked Auditory Brainstem Response (eABR), and determine if cochlear implantation was required. Clinical question: How significant was intraoperative eABR in determining the outcome of cochlear implantation? Case report: This study considered two cases with profound bilateral SNHL that underwent intraoperative eABR. The first case involved 10-year-old girl who had used conventional hearing aids for eight years before surgery. She practiced lip reading for communication. The second case involved 4-year-old boy with delayed speech and a history of febrile seizure when he was two years old. He had used a conventional hearing aid for six months. Method: Evidence based literature was conducted through PubMed, Embase, and Wiley. Result: On the first case, eABR examination evoked no response in both ears and the parents decided not to carry on with the surgery. In the second case, eABR examination aroused a significant response in both ears, so the implantation was performed. Three months postoperative, the child was babbling and able to detect sound. Conclusion: eABR could give valuable input in identifying profound bilateral SNHL patients with cochlear nerve abnormality. The high cost of implant devices makes this examination beneficial for the patient’s family in deciding if implantation surgery is required. Keywords: cochlear implant, cochlear nerve hypoplasia, eABR, hearing habilitation, profound sensorineural hearing loss

Title

Found 10 Documents
Search

Abstract

Abstract

Abstract

Abstract

Abstract

Abstract

Abstract

Abstract

Abstract

Abstract

Title Search

Found 10 Documents Search

Abstract

Abstract

Abstract

Abstract

Abstract

Abstract

Abstract

Abstract

Abstract

Abstract

Title

Found 10 Documents
Search