Detty Siti Nurdiati
Department Of Obstetrics And Gynecology, Faculty Of Medicine, Public Health And Nursing, Universitas Gadjah Mada/Dr. Sardjito General Hospital, Yogyakarta, Indonesia

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Journal : Nusantara Medical Science Journal

A Rare Case of Conjoined Pygopagus Twins: Case Report Saputro, Christina; Siti Nurdiati, Detty; Taufiqur Rachman, Irwan
Nusantara Medical Science Journal Volume 8 Issue 1, January - June 2023
Publisher : Faculty of Medicine, Hasanuddin University.

Show Abstract | Download Original | Original Source | Check in Google Scholar | DOI: 10.20956/nmsj.v8i1.19690

Abstract

Introduction and importance: Conjoined twins are a complication of monozygotic pregnancies with an incidence of 1:50,000-200,000 of life births. Pygopagus is found around 17% of all types of conjoined twins and has a mortality rate of 23%. Proper diagnosis and management in this case is important. Presentation of case: A 25-year-old primigravida woman presented at 22 weeks of gestation with a Pygopagus ultrasound result at 17 weeks of gestation. MRI was performed at 25 weeks of gestation, showed conjoined pygopagus twins with lumbosacral spina bifida, without visualized bone union, separated bladder, rectum and anus were difficult to evaluate. Caesarean section (CS) is planned at 36 weeks of gestation and postpartum MRI will be performed in preparation for the separation surgery. The patient was admitted to the hospital at 35 weeks of gestation in the active phase of the first stage of labor, then an urgent caesarean section was performed. Both babies were born with an APGAR score of 2/4/7. The second baby died a few hours after delivery. The separation surgery was performed as an emergency, but the first baby died during the procedure. Conclusions: Pygopagus requires holistic management, starting from diagnosis, preparation for delivery, to postpartum complications. The proper holistic management is expected to reduce infant and maternal morbidity and mortality.
Co-Authors - Pujiatun Adi Rahmawan Adi Rahmawan, Adi Agung Dewanto Ahsanudin Attamimi Alifia Salsabila Amdad Amdad Amelia, Dwirani Anggoro Budi Hartopo Anindya K Zahra Anis Widyasari Anjarwati Anjarwati Anjarwati Anjarwati, Anjarwati Ari Purwoko Widji Utomo Armalya Pritazahra Asri C. Adisasmita Atik Tri Ratnawati Atik Triratnawati Budi Arianto Budi Arianto, Budi Cahyawati, Safitri Putri Darwin Nasution Depari, Irmanda Terbelluh Sembiring Dessy Hertati Dewanto, Agung Dewi Rokhanawati Dewi Rokhanawati, Dewi Dhesi Ari Astuti, Dhesi Ari Dhesy Ari Astuti Dhesy Ari Astuti, Dhesy Ari Diah Rumekti Hadiati Diannisa Ikarumi Enisar Sangun Djaswadi Dasuki Dyah Wulan Anggrahini Eka Rati Astuti Ely Yulianus Musa Limbu Emy Huriyati Erna Ashlihah Rochmat Eugenius Phyowai Ganap Fajarini, Yuniar Ika Fauzan Achmad Maliki Febriana Sari Febriana Sari, Febriana Fika Humaeda Assilmi Fitri Haryanti Fitriana K, Herlin Fitriana K., Herlin Ganap, Eugenius Phyowai Hamam Hadi Herlin Fitriana K Husnah Husnah Indria Laksmi Gamayanti Indria Laksmi Gamayanti Intan Agustina Anggraeni Irmitasari Irmitasari Irmitasari, Irmitasari Irwan Taufiqur Rachman Iswanti, Tutik Iswanti1, Tutik Johariyah - Johariyah Juli Sitorus Kamsiah . Kartika Wahyuningtyas Utami Kemal N. Siregar Khairina Hashifah Khrisnamurti, Sinta Kristiana Tri Warsini Kusuma, Raden Aditya Lidia Aditama Putri Linda Shintiana Lisma Evareny, Mohammad Hakimi, Retna Siwi Padmawati Lucia Kris Dinarti Mae Sri Hartati Wahyuningsih Mohammad Hakimi Muhammad Gahan Satwiko Muhammad Nurhadi Rahman Muhammad Reyhan Hadwiono Musa Limbu, Ely Yulianus Nasution, Darwin Noer Saudah Noer Saudah, Noer Nu Pravitasari Nur Falah Setyawati Nur Khamidah Nuring Pangastuti Ori Pertami Enardi Ova Emilia Pramudji Hastuti, Pramudji Prihesti, Uce Siswi Priyatin Sulistyowati Rachmawati Widyaningrum Ratna Widhiastuti Retty Nirmala Santiasari . Ririn Ariyanti Ririn Ariyanti, Ririn Saidah Agustina Sucipto Putri, Noer Elvi Saputro, Christina Sarah Ayu Andari Setiarsih, Dini Setiyarini, Wahyu Ikka Shintiana, Linda Sinta Khrisnamurti Sitorus, Juli Sitorus, Melina Ebtarina Sitorus, Melina Ebtarina Sri Juana Sri Restu Sulchan Sofoewan Sulchan Sofoewan, Sulchan Sulistyaningsih, Sulistyaningsih - Sumarni Sumarni Sumarni Sumarni Tutik Iswanti Uce Siswi Prihesti Untung S. Widodo Utomo, Muhammad Wahyu Vera Dewanto Wahyu Ikka Setiyarini Wahyu Ikka setyarini Wahyu Widayati Wahyu Widayati, Wahyu Widyaningrum, Rachmawati Widyawati Widyawati Widyawati Widyawati Wiwin Lismidiati Wulandari, Andhyta Ratih Yanuarti Petrika Yayi Suryo Prabandari Yuniar Ika Fajarini