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Journal : JOURNAL LA MEDIHEALTICO

Mucous Membrane Pemphigoid: A Frustrating Disabling Disease in A 15-year-old Male Akhyar, Gardenia; Izrul, Irdawaty; Nagara, Adianto Jaya
Journal La Medihealtico Vol. 5 No. 1 (2024): Journal La Medihealtico
Publisher : Newinera Publisher

Show Abstract | Download Original | Original Source | Check in Google Scholar | DOI: 10.37899/journallamedihealtico.v5i1.1078

Abstract

Mucous membrane pemphigoid (MMP) is a rare chronic autoimmune subepithelial blistering disease characterized by erosive lesions of mucous membranes and skin that typically results in scarring of at least some sites of involvement. A progressive disorder that may result in serious complications including blindness, loss of the airway, and esophageal stricture formation. Most patient experience reduced quality of life specifically with ocular symblepharon and laryngeal destruction. Case: We present a case of a 15-year-old male patient with 1 month-history of multiple tense bullae, difficulty to open the eyes, and hoarseness due to scar lesion in mucous membrane. The patient was reported to have Dermatology Life Quality Index (DLQI) of 15 which implied he had severe disability and decreased quality of life due to his illness. Patient also had symblepharone release operation done by ophthalmologist. A laryngeal reconstruction plan was also carried out by ENT doctor, but the patient couldn’t continue the treatment because of economic problem. Scarring of MMP is a significant complication in many cases. Mucous membrane pemphigoid could cause a lot of disability to the patient and decreased quality of life. Symblepharone release operation was done and laryngeal reconstruction plan was also carried out. Surgical intervention may not curable; however, it may be necessary for restoring function and improving quality of life.
Co-Authors Abdiana Abdiana, Abdiana Adissa Benanda Afdal Afdal, Afdal Afdhila , Irhamni Nur Afriani, Nita Agustin Vira Agustin Vira Alimuddin Tofrizal Alvarino Alvarino Amel Yanis Amelin, Fitrisia Andani Eka Putra Andrini Ariesti Andrini Ariesti Anum, Qaira Ashal, Taufik Asri, Ennesta Astria Rima Rara Yuswir Astria Rima Rara Yuswir Benanda, Adissa Cimi Ilmiawati, Cimi Dedy Kurnia Desmawati Desmawati Desviorita, Rika Endrinaldi Ennesta Asri Ennesta Asri Erlina Rustam Fathiyyatul Khaira, Fathiyyatul Fauzana Nazifah Fikri Fadhil Fortuna, Fory Gusti Revilla Hendriati, Hendriati Husna, Annisa Tamara Husna, Annisaul I. Izrul Ida Rahmah Burhan Indah Indria Sari Indah Indria Sari Irdawati Izrul Irdawaty Izrul Irhamni Nur Afdhila Izrul, Irdawaty Jefrizal Wirman Julita Julita Julita Julita Julizar Julizar Kemala Sayuti Kurnia, Dedy Lestari, Rahmi M. Ashar Maimi, Afaf Aqil Mardhiati Mardhiati Masrul Meligasari L Gaya Muhamad Firdaus Mutia Sari Nagara, Adianto Jaya Nailatul Fadhila Netti Suharti, Netti Novian Novian Novian Novian Nur, Fauziah Nurul Izzah Putri, Biomechy Oktomalio Rahma Ledika Veroci Raveinal Rendra Darma Satria Rendra Darma Satria Rika Desviorita Rika Desviorita Rina Gustia Rina Gustia Riri Prima Yolanda Rizki Dwayana Rizki Dwayana Rizkia Chairani Asri Salwa Azzahra Satya Wydya Yenny Selfi Renita Rusjdi Shafiqah Zawira Syamel Muhammad Tiffany, Begum Tofrizal Tutty Ariani Tutty Ariani Vesri Yossy Vitresia, Havriza Yenni Raflis Yola Fadilla Yosse Rizal Yulistini, Yulistini Yusticia Katar Yustini Alioes Zafira, Qory