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Journal : Alami Journal (Alauddin Islamic Medical) Journal

Nutritional Therapy in Adult Hirschsprung Disease Post-Total Colectomy and Ileostomy with Severe Protein-Energy Malnutrition: A Case Report Faradilah, Andi; Christine Rogahang; Nurbaya Syam; Agussalim Bukhari
Alami Journal (Alauddin Islamic Medical) Journal Vol 9 No 2 (2025): JULY
Publisher : Universitas Islam Negeri Alauddin Makassar

Show Abstract | Download Original | Original Source | Check in Google Scholar | DOI: 10.24252/alami.v9i2.60167

Abstract

Adult Hirschsprung disease, also known as congenital aganglionic megacolon, is a rare congenital disorder characterized by the absence of ganglion cells in the distal segment of the large intestine, diagnosed in adulthood. Impaired nutrient absorption due to the dysfunctional intestinal segment can lead to malabsorption and malnutrition. A 23-year-old female presented with severe protein-energy malnutrition after total colectomy surgery for suspected adult Hirschsprung disease. She had a history of chronic constipation from childhood, abdominal pain, and abdominal distension. She was referred to a clinical nutritionist 2 days post-surgery. The nutrition therapy started with oral and parenteral nutrition, gradually increasing macronutrient requirements based on clinical condition and gastrointestinal tolerance.  On the 12th day post-total colectomy surgery, she developed complications of obstructive ileus, requiring ileostomy. Laboratory tests showed signs of inflammation. Nutritional support for adult Hirschsprung disease focuses on meeting energy requirements, enhancing nutrient absorption after abdominal surgery, and minimizing post-operative inflammation.
Co-Authors A. Yasmin Syauki A. Yasmin Syauki Ahmad, Mardiana Alfina Baharuddin Aminuddin Aminuddin Aminuddin Aminuddin Amru, Khaeriah Andi Alfian Zainuddin Andi Asadul Islam Andi Hariati Bachtiar Andi Nilawati Usman Andi Syurma Sari Ismail Anton Anton Anton, Sri Sulistyawati Arbie, Rina Sulisthia Ari Andini Junaedi Aryanti R Bamahri Aryanti R. Bamahry Asih, Puji BS. Asrini Safitri Asrini Safitri Bachtiar, Andi Hariati Baharuddin Baharuddin Baso, Aidah Juliaty A Budu - Burhanuddin Bahar Christine Rogahang Citra Kesumasari Daud, Nurpudji Astuti Din Syafruddin Djaharuddin, Irawaty Ema Alasiry, Ema Faradilah, Andi Fatmawati Nur Husain Ferry Sandra Firdaus Hamid Haerani Rasyid Haerani Rasyid Halik, Handayani Hasyim, Ammar A. Healthy Hidayanty Hidayanty, Healthy Ibrahim Labeda Ilhamjaya Patellongi Ilmianti, Ilmianti IRFAN IDRIS Itani, Kei Iyori, Mitsuhiro January, Rima Josephine Thewakan Kadek Ayu Erika Karnely, Karnely Khairuddin Djawad Maisuri T Chalid, Maisuri T Makmun, Armanto Marcellus Simadibrata Mardiana Madjid Maria Ingrid Budiman Meta Mahendradatta Mia Miranda Mochammad Hatta Mochammad Hatta Muh. Nasrum Massi Nakamura, Kurumi Nanang Wiyono Natalia Rorrong Pamilangan Ni Luh Puti Herli Mastuti Nur Ashari Nurbaya Syam Nurbaya Syam Nurhadi, Asty A. Nurisyah, Sitti Nurpudji A. Taslim Nurpudji Astuti Taslim Parewangi, Muhammad Luthfi Prihantono Prihantono R Satriono R Sutrisno Rabiah Rabiah Rahmani, Muhammad Z. Ratnaeni Rina Masadah Rinda Nariswati Rosdiana Natzir Rosdiana R Sri Ramadhany Sri Wahyu St.Pasriany Suryani As’ad Suryani As’ad Syarif, Isymiarni Taslim, Nurpudji Astuti Tawali, Suryani Tjahjadi Robert Tedjasaputra Umrayani Veni Hadju Veni Hadju Warmayana, I Gede Agus Krisna Yoshida, Shigeto Yusuf Yenni Zainal, Kartika H.