Evy Ervianti
Departement Of Dermatology And Venereology, Faculty Of Medicine Universitas Airlangga/Dr. Soetomo General Academic Hospital, Universitas Airlangga Teaching Hospital, Surabaya

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Journal : Asian Journal of Health Research

Cutaneous Manifestations of Scleroderma: A Case Report Tessa Thendria; Amira Suryani Rahmatika; Evy Ervianti; Dwi Murtiastutik; Trisiswati Indranarum; Hasnikmah Mappamasing; Septiana Widyantari
Asian Journal of Health Research Vol. 2 No. 2 (2023): Volume 2 No 2 (August) 2023
Publisher : Ikatan Dokter Indonesia Wilayah Jawa Timur

Show Abstract | Download Original | Original Source | Check in Google Scholar | DOI: 10.55561/ajhr.v2i2.103

Abstract

Background: Scleroderma or systemic sclerosis is a rare multisystemic autoimmune disease characterized by vasculopathy, inflammation, and progressive fibrosis of the skin and multiple organs. Cutaneous manifestations and Raynaud’s phenomenon, usually becomes the initial presentation of scleroderma which noticed by the patient. Case: A 47-year-old-women presented with hardened and thickened skin on her arms and legs for 3 years which spreaded to her face and trunk. The lesions initially appeared as multiple red patches which progressed into white, thick and hard patches. The patient had history of recurrent Raynaud's phenomenon, dry cough, and shortness of breath. In the physical examination, the patient had skin hardening with salt and pepper appearance on her upper back and chest. The thoracic CT scan revealed interstitial lung disease. The patient diagnosed as definitive scleroderma based on The European League Against Rheumatism (EULAR)/American College of Rheumatology (ACR) criteria with score of 18. She has treated with methotrexate, methylprednisolone, topical corticosteroid and moisturizer. The skin lesion improved with the reduction of Rodnan skin score from 31 to 19 after 4 months of treatment. Conclusion: Cutaneous manifestation could be the early alarm and initial manifestation of scleroderma. As the pathology is deep beyond the skin, throughout examination should be performed to find any organ involvement. Dermatologist play a significant role in early identification of skin disorder and made multidiciplinary refferal. Early diagnosis and prompt treatment could reduce morbidity and mortality in scleroderma
Co-Authors Addia Salsabila Ade Fernandes Ade Fernandes Afif Nurul Hidayati Afif Nurul Hidayati, Afif Nurul Ahmad, Zahruddin Alphania Rahniayu Amanda Gracia Manuputty Amira Suryani Rahmatika Amira Suryani Rahmatika Anang Endaryanto Anggraeni, Sylvia Astindari Astindari Astindari Astindari Astindari, Astindari Axelia, Presstisa Gifta Azzahra, Safira Bagus Bagus Bagus Haryo Kusumaputra Bagus Haryo Kusumaputra, Bagus Haryo Bagus Meurah Suropati Bernadya Yogatri Anjuwita Budi Prasetyo Budi Utomo BUDI UTOMO Budi Utomo Budiono Budiono Budiono Budiono budirahmadina, nurvania aurellia Chesia Christiani Liuwan Cindy Fransisca, Cindy Cita Rosita Sigit Prakoeswa Damayanti Damayanti Damayanti Damayanti Damayanti Damayanti Damayanti David Sontani Perdanakusuma Dewi Puspitorini Diah Mira Indramaya Diah Nugrahaeni Diah Nugrahaeni, Diah Dwi Murtiastutik Dwi Nurwulan Pravitasari Dyatiara Devy Rahadiyanti Dyatiara Devy Rahadiyanti Eko Budi Koendhori, Eko Budi Ellenita Soebakti Endang Wahyu Fitriani Esthy Yuliana Esti Hendradi Fadila, Arisia Faizah, Wardatun Farhat Surya Ningrat Fatma Rosida Frizka Eliza Geani, Silvani Hadiwidjaja, Farsha Naufal Hamidah Luthfidyaningrum Hans Lumintang Hans Lumintang, Hans Harith Ali Al-Taie Harningtyas, Citra Dwi Hasnikmah Mappamasing I Gusti Ayu Agung Elis Indira I Gusti Nyoman Darmaputra Indah Purnamasari Indah Purnamasari Indiarsa Arief L Indiarsa Arief L, Indiarsa Arief INDROPO AGUSNI Intan Primasari Irmadita Citrashanty Irmadita Citrashanty Irmadita Citrashanty, Irmadita Iskandar Zulkarnain Iskandar Zulkarnain Kathrin Kezia Henry Kawilarang, Arthur Pohan Kurniati Kurniati Linda Astari, Linda Lunni Gayatri Lunni Gayatri, Lunni M. Kharis Khamdan M. Yulianto Listiawan Made Putri Hendaria ManikRetno Wahyunitisari Mappamasing, Hasnikmah Maria Ulfa Sheilaadji Marsudi Hutomo Maylita Sari Maylita Sari Maylita Sari, Maylita Medhi Denisa Alinda, Medhi Denisa Menul Ayu Umborowati, Menul Ayu Mikiyas Gifawosen Teferi Nadya Kelfinta Hanani Ngesti Kumalasari, Diah Nugroho, Wisnu Triadi Nur Khamidah Nurul Wiqoyah, Nurul Nyoman Suryawati Pepy D. Endraswari Pepy Dwi Endraswari, Pepy Dwi perdanakusuma , david sontani Pinem, Veronica Abebia Beginanta Pratiwi, Karina Dyahtantri Priangga Adi Wiratama Puspowati, Erindah Rahmadewi Rahmadewi Rahmadewi Rahmatika, Amira Suryani Rebekah Setiabudi, Rebekah Regitta Indira Agusni Retha Retha Riezky Januar Pramitha Rubianti, Marissa Astari saputra, iswinarno doso Sari, Desiana Widityaning Sawitri Sawitri Sawitri Sawitri Sawitri Sawitri Sawitri Selvia Yuliani Dwi Ratih Sanggarwati Septiana Widyantari Septiana Widyantari Shakti Indraprasta Sheilaadji, Maria Ulfa Sulaksanaswastho Suyoso Sunarso Suyoso Sunarso Suyoso Sunarso Suyoso Sunarso Suyoso, Sunarso Sunarto, Olivia Awwalin Tanojo, Natalia Tengku Riza Zarzani N Tessa Thendria Tjokorde Istri Nyndia Vaniari Trisiswati Indranarum Trisniartami Setyaningrum Wardiana, Maya Wisnu Triadi Nugroho Yoana Fransiska Wahyuning Christi Yuindartanto, Andre Yuri Widia, Yuri Yuri Widya Yusuf Wibisono