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Journal : Heart Science Journal

Pregnancy in patient with congenitally corrected transposition of the great artery and ventricular septal defect without pulmonary stenosis: A case report Auliya, Faiza Fardha; Bambang Rahardjo; Indrawan, I Wayan Agung
Heart Science Journal Vol. 6 No. 4 (2025): The Pursuit of Precision: Navigating Risks, Refining Diagnosis, and Securing Lo
Publisher : Universitas Brawijaya

Show Abstract | Download Original | Original Source | Check in Google Scholar | DOI: 10.21776/ub.hsj.2025.006.04.17

Abstract

Background: Transposition of the Great Arteries (TGA) is a congenital heart defect affected by an embryological misalignment between the aorta and pulmonary trunk. Congenitally Corrected Transposition of the Great Arteries (CCTGA) or L-TGA, accounts for less than 1 % of congenital cardiac disease cases. This report presents the case of a pregnant woman with a history of CCTGA who successfully delivered an infant. Case illustration: A 32-year-old woman presented with vaginal bleeding at 30-32 weeks of gestation and a history of CC-TGA. Her medical history included CCTGA, ventricular septal defect (VSD) without pulmonary stenosis, prior molar pregnancy curettage, breech fetal position, moderate acute respiratory distress syndrome (ARDS), and low body mass index (BMI 16.6 kg/m²). She was classified as WHO Cardiac Risk Class IV due to the high risk of maternal mortality. Following corticosteroid administration for fetal lung maturation and multidisciplinary evaluation, a planned cesarean section was performed at 30 weeks. A male infant was delivered, weighing 1,480 grams, measuring 41 cm in length, with Apgar scores of 7 and 9, and a Ballard score of 18. Conclusion: Early risk assessment, multidisciplinary collaboration, and individualized management are pivotal in reducing maternal and fetal morbidity in patients with CC-TGA.
Idiopathic Pulmonary Arterial Hypertension Newly Diagnosed in Pregnancy with Anemia and Threatened Preterm Labor Harumsari, Stefani; Rahardjo, Bambang; Prasetyorini, Nugrahanti; Dwijayasa, Pande Made; Yogibuana, Valerinna; Rohman, Mohammad Saifur
Heart Science Journal Vol. 3 No. 4 (2022): Prevention, Screening dan Rehabilitation : The Back Bone of Quality Care Improv
Publisher : Universitas Brawijaya

Show Abstract | Download Original | Original Source | Check in Google Scholar | DOI: 10.21776/ub.hsj.2022.003.04.7

Abstract

Background: Pulmonary hypertension (PH) is a rare cardiovascular disorder that leads to right heart failure (RHF). Although most PH occurs secondary to congenital heart disease (CHD), PH can occur primarily due to pulmonary arterial vasculature abnormalities, known as Idiopathic pulmonary arterial hypertension (IPAH). In addition, the physiologic changes during pregnancy can potentially lead to worsening PAH and confer a poor prognosis. Therefore, when the mother refuses termination, a multidisciplinary team should manage the pregnancy and delivery to improve maternal and fetal outcomes.Objectives: This case report aimed to describe the importance of early diagnosis and treatment in PAH.Case reports: We reported a case of a 24-year-old woman with idiopathic pulmonary arterial hypertension (IPAH) that was newly diagnosed at 25 weeks of pregnancy and previously misdiagnosed with patent ductus arteriosus (PDA). This pregnancy was complicated with anemia and threatened preterm labor. Sildenafil was used as a vasodilator to reduce the symptoms of PAH. Unfortunately, the pregnancy was terminated at 29 weeks because of PPROM after considering giving lung maturation and neuroprotectant to the fetus. The patient was discharged without complication, but the baby died after eight days of intensive care due to HMD II, which led to respiratory failure.Conclusion: PAH in pregnancy is a life-threatening condition if untreated. Continuous treatments can help control the symptoms and avoid further complications for both mother and baby.
Co-Authors A.A. Santi Dewi Abd. Rasyid Syamsuri Agustina Tri Endharti Aldiansyah, Dudy Aldika Akbar, Muhammad Ilham Alim, Fathi Nabila Aloysius Suryawan Amir, Nayla Nabilla Tahta Avwina Andonotopo, Wiku Anggie Diniayuningrum Anggraeni, Yessy Mulyanur Anik Sri Purwanti Anin Indriani Anisa Setyowati Anita Dwi Rahmawati Annisa Jusuf, Annisa Annissa Febriani Ariani, Novida Astuti, Ludji Auliya, Faiza Fardha Aziz, Ali Bachnas, Muhammad Adrianes Baihaqi, Irfani Cholid Tri Tjahjono Cut Meurah Yeni Daniati, Lidya Dewi Azar Nuria Wardani Dewi, Ratih Frastika Diadjeng Setya Wardani Dinda Oktia Maghfiroh Edy Mustofa Erna Amin Evert Solomon Pangkahila Fauqo Wildatil Jannah Gusti, Kharisma Ciptaning Harumsari, Stefani Hery Setiawan, Hery Hidayat Sujuti Hikmawan Wahyu Sulistomo I Nyoman Hariyasa Sanjaya I Wayan Agung Indrawan I Wayan Subage Ihda Dian Kusuma Ihda Dian Kusuma Indrayanti Indrayanti Indriani, Anin Indriati Dwi Rahayu Irfani Baihaqi Ita Sulistiani Julian Dewantiningrum Kalsumy, Umi Kharisma Ciptaning Gusti Kurjak, Asim Kusworini Handono Lestari, Ni Putu Yunita Sri Lilik Zuhriyah Ludji Astuti Melani Chysti Situmorang Mohammad Saifur Rohman Mosip, Erinus Mukhamad Nooryanto Noviyanti Noviyanti, Noviyanti Nugrahanti Prasetyorini Nur Sophia Matin Nurdiana Nurdiana Nurdiana Nurdiana Nurdiana Nurdiana Nurseta, Tatit Nuswil Bernolian Pande Made Dwijayasa Permatasari, Galuh W. Pramono, Mochammad Besari Adi Pratama, Harry Dwi Purba, Irene Silvia Purbandari, Rosalia Puspita Handayani Putra, Ichsan Setya Regina Ayu Fristiyanti Rizki, Mutiara Putri Nanda Rizki, Mutiara Putri Nanda Ryan Saktika Mulyana Sabilla Khaerunissa, Dymphna Safrina Dewi Ratnaningrum Sanarto Santoso Sanggelorang, Margie Cassie Setyowati, Anisa Sirat, Noorhamdani A. Siti Candra Windu Baktiyani Siti Candra Windu Baktiyani Situmorang, Melani Chysti Sri Poeranto, Sri Sri Sulistyowati Sri Winarsih Stanojevic, Milan Subandi Subandi Sugiono, Achmad Sulistiani, Ita Sulistomo, Hikmawan Wahyu Sultanah Zahariah Sumarno . Sumarno Sumarno Sururi, Desy Aulina Sururi, Desy Aulina Sutrisno Sutrisno Talita Nandia Primarintan Tatit Nurseta Tatit Nurseta Theresia Monica Rahardjo Udjianto, Udjianto Wardani, Dewi Azar Nuria Wardani, Widya Kusuma Wati, Linda Ratna Wibisono, Hermawan Widyalaksono, Agung Winasih, Sri Wiradnyana, Anak Agung Gede Putra Wiyasa, I Wayan Arsana Yahya Irwanto Yogibuana, Valerinna Yuyun Yueniwati Zahariah, Sultanah