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Journal : Medical and Health Science Journal

Navigating the Uncommon: Case Report of Arrhythmogenic Right Ventricular Cardiomyopathy (ARVC) Successfully Managed with Implantable Cardioverter Defibrillator (ICD) Purwowiyoto, Sidhi Laksono; Hermawan; Kusharsamita, Hillary
Jurnal Ilmu Kesehatan dan Kesehatan Vol 8 No 02 (2024): AUGUST
Publisher : UNUSA Press

Show Abstract | Download Original | Original Source | Check in Google Scholar | DOI: 10.33086/mhsj.v8i02.5666

Abstract

With a high risk of sudden cardiac mortality, arrhythmogenic right ventricular cardiomyopathy (ARVC) is a rare inherited cardiomyopathy characterized by right ventricular dysfunction and ventricular arrhythmias (VA). In this case study, a 35-year-old presented with palpitations and revealed epsilon waves on the right precordial electrocardiogram (ECG) leads which led to the suspicion of ARVC. A 24-hour Holter monitoring revealed frequent ventricular extrasystoles (>500 per 24 hours), a CMRI revealed RV dyskinesia and transmural LGE in the apical RV, and an electrophysiologic study detected spontaneous polymorphic ventricular tachycardia (VT) despite the presence of induction ventricle fibrillation (VF). These results validated the diagnosis of ARVC and indicated that an implantable cardioverter defibrillator was necessary treatment. The ability to identify potential ARVC’s ECG abnormalities, the timing to pursue further studies, and determining necessary treatment execution are critical. The evaluation of cardiac, electrophysiological, and clinical imaging parameters is essential for the risk stratification, diagnosis, and management of patients with ARVC.
Co-Authors Abdul Hamid Abu Khurairoh Achmad Firman Adnen Bait Sabila Adriana Sari Aryani Afifah, Fauzia Nur Afrilda Rakhma Yusanty Agustiansyah, Putra Ahmad Irfa’i Ahmad Mirza Alfa Khusni Ajat Sudrajat Al Ashar, Ilham Ariawan Alif Dido Wijoseno Amalia Bahri2, Lola Andri Anggia Putri, Meliani Anjarwani, Ratih Ariadi, Seno arianti, rita Astono, Anjar Dwi Astria Nur, Hana Aulia, Destia Afta Bamualim, Mubarak Bayu Anggara Bryan Brama Ramadhana Budi Setiadi Cahyo Priyo Sembodo Christi, Raden Febrianto Dara Salsabila Rianti Dewi Candra Resmi Dharma, Andhika Guna Dinar Munggaran Ahmad Eva Fatayatul Mufidah Fajar Budiman, Fajar Farkhan, Anindya Farkhatus Sakila Faza Syiham Mu’afa Febriana Putra, Bimas Febrianto Christi, Raden Feris Dzaky Ridwan Nafis Fitri, Abimanyu Kusuma Nur Fitri, Anisa Gatot Yulianto Gusti Ilman Prayoga Haifa Ersa Salsabila Hana Astria Nur Hana Astria Nur Hartono, Daniel Hendriani, Adinda Septi Herman Susilo hidayat, Muslim Ika Norma Nafisa Ilham Ferdiansah, Muhamad Ilham Setiaji, Galih Ilham, Ilham Ariawan Al Ashar Imam Abdul Aziz Aziz Indrawati Aris Tyarini Iskarimah, Rizqi Iskarimah Isra Djabbar JAMALUDIN Jenny Febrina Andini Joko Setiawan Kotim Subandi Kusharsamita, Hillary Kusumah, Rita Kusumawati, Diah Tri Lia Budimulyati Salman Lidya Fauziyah Lisna Oktaviani Mahanani, Seia Maharani Maria Wahyuni Masnur Ali Meia Salina Lestari Moh Nur Amin Mohammad Anwar, Mohammad muhamad Fuat Asnawi Muhammad Fathi Ulumuddin Muhammad Herjendi, Aldianur Muhammad Rafli Musafa Hudin Muslim Muslim Hidayat Nadia Luthfiyanti Zahra Nahar Mardiyantoro NASRUDIN Ngatoilah, Mohamad Ningsih, Asih Ria Ni’ma Nuzulan Idznillah Nofrita, Misra Nugraha, Hartman Nulngafan Nurahman, NI Nuratika Nuriana Hifzha Syiva Nurul Hidayat , Rizza Nurwijayanti Oman Hadiana Oscha Davan Kharisma Permata Sari , Devi Prasetio Adi, Danang Purwanto Purwowiyoto, Sidhi Laksono Putri Dela Asyfa R. Arya Rahmadiyatmaka Raden Febrianto Christi Raka Imam Rachmawan Reni Sulastri Ria Ningsih, Asih Ricky Firmansyah Rifai, Nurdin Rina Nuraisyah Rismawati Rismaya Robi Sutana Putra Roestamy, Martin Rohhani, Imam Rosinda Saubig, Arnila Novitasari Setyo Nugroho Haribowo Sobandi, Iban Sofyan, Arif Sopian Stefanie Virlanta Putri Stelina Candita Gunawan Sin Sin Tan Sudirman Baso Sukowiyono Susilotami, Rifa Khoirunnisa t Budi Utomo, S. Slamet Tegar Wirasatya Al Ashar, K Victor Ilyas Sugara Wahdaniah, Wini WINARTO Yeni Haerani, Yeni Yohanes Yuli Mulyanto