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Journal : Action Research Literate (ARL)

Herlyn-Werner-Wunderlich Syndrome: Challenges in Early Diagnosis Natasha, Ayu; Punarbawa, Gede; Noviyanti
Action Research Literate Vol. 9 No. 6 (2025): Action Research Literate
Publisher : Ridwan Institute

Show Abstract | Download Original | Original Source | Check in Google Scholar | DOI: 10.46799/arl.v9i6.2973

Abstract

Herlyn-Werner-Wunderlich syndrome (HWWS) is a rare Müllerian duct anomaly characterized by the triad of uterine didelphys, blocked hemivagina, and ipsilateral renal agenesis. The syndrome often remains asymptomatic until after menarche, when symptoms related to haematocolpos, such as severe dysmenorrhea, become apparent. This study presents a case of a 14-year-old female who presented to the Urogynecology Department with complaints of severe dysmenorrhea. Diagnosis was confirmed through CT scan and ultrasound imaging, which revealed the typical triad of HWWS. The treatment involved the surgical incision of the vaginal septum to address the obstructed hemivagina. While HWWS is usually diagnosed after the onset of menstruation due to the development of haematocolpos, early detection during infancy could help prevent acute complications. The study emphasizes that gynecologists should consider HWWS in the differential diagnosis when patients present with cyclic pelvic pain, monthly alterations in menstrual flow, pelvic masses, or renal agenesis. Early identification and management of HWWS are crucial to prevent long-term complications.
Co-Authors Agus Prasetyawan Ainy, Afra Nur Amalia , Rosemila Amalia, Rosemila AMBAR WIDYA LESTARI Andriani Angga Domeos Manggara Antonio Constantino Soares Ari Widyaningsih Arianti, Gisela Arnando Asma, Nurul ASNI Asterina, Yolanda Aulia Rosida, Nabila Azizah, Maulia Salsanabila Azwar, Yessi Badrudin Kurniawan Basuki Batubara, Hamidah Sari Bella, Ivvon Septina Berliani, Dedek Bunga Tiara Carolin DIAN ARLUPI UTAMI Dirgayusa Febrianaga, Pipit Eliyah Emy Susanti EVA AULIA MUKTI Eva Tresanita Damanik Faisal R Dongoran, Faisal R Fitrianingrum, Aditya Pratiwi Florida Gading Gamaputra Handayani, Sri Hidayatullah, Agus Hikmah, S.E., M.Si. Hutasoit, Eva Santi Ice Irawati Imanudin Siregar Indah Puspitasari Indera Hayati, Aulia Dian Isnaini Fitri Effendi Jayanti Juliani, Wahyuni Karimah, Arzetya Fitri Al Keristanti, Ruri Khairunnisa, Anita Khummad Robby, Tasbikhy Kusuma Dewi, Novian Leni Utami Lina Haryani Lukmawati, Luthfi Rizky Mar'atus Sholikhah Maratun Shoaliha Matulessy, Stella Maria Mauizatul Hasanah Maulida Mega Dewi Lestari Meissi Kusuma Wardhani Melgita Sari Nurjayanti Saputri Melisa Misriningsih, Dwi Cahyani Muhammad Zaini Mur'ah Murni Murniati Nanik Cahyati Natasha, Ayu Naufal Hanif Ramadhan Norwanda Nur Rachma, Dita Laela Nurkhairina Nurlina Nurmayana Nurwahidah, Andi Tenri Oskar Pardosi, Renhad Andreas Permana, Handy Januar Pinata, Putri Prasetyo Isbandono Punarbawa, Gede Purnamasari, Ade Irma Putri Fatahillah, Ratu Egalitarian Ranti Widayanti Ratna Sari, Monika Retno Widuri, Aliffionia Sindy Hendrati Rice Haryati Rinanti, Maghalita Rinanti Rita Dewi Triastianti Rizka Hadya Robby Cokro Buwono Rosyidah, Neneng Aida Salinan Sarasati, Inda Siti Maesaroh Sophia Sri Mustika Sujarwo Putri, Tarisa Sukarsono, Faza Muhammad Suwiase, Putu Syalmah Tahlia Wahyuning Tias Takharus Awal, Annisa Zahra Tanosida K Tohidi, Edi Triatmi Sri Widyaningsih Wahyuni, Rika Sri Warsiyah Warta, Waska Wati, Norlidia WENI ROSDIANA Wibisono, Haryo Kunto Widyaningtyas, Dwi Wilujeng, Vianti Winata, Muhammad Danu Yekti Murbarani Yeni Rosyeni Yulistia Yuni Lestari Yuni Lestari Yusuf, Salsabila Zalikha Zulfahmi